1033: Congenital Considerations: Mounier-Kuhn Syndrome and Recurrent Pneumonia
نویسندگان
چکیده
منابع مشابه
Mounier Kuhn syndrome presenting with recurrent atelectasis.
Objective and importance Mounier Kuhn syndrome is usually diagnosed in adulthood, and only a few cases have been described in childhood. Clinical presentation We present the case of a seven-year-old boy suffering from recurrent pneumonia and atelectasis. Intervention Previously performed chest X-rays showed bilateral hyperinflation and tracheobronchomegaly. Chest computed tomography (CT) confir...
متن کاملTracheobronchomegaly (Mounier-Kuhn Syndrome)
Tracheobronchomegaly (Mounier-Kuhn syndrome) is defined as marked cystic tracheobronchial dilatation. Tracheobronchomegaly (TBM) is a rare condition primarily effecting men between the ages of 40 to 50 years. The etiology of TBM is unknown. Pathologically, there is atrophy of the muscular and elastic elements of the trachea and central bronchi. The diagnosis of TBM and the associated pathology ...
متن کامل[Mounier-Kuhn syndrome].
Departments of 1. Radiology and 2. Pneumology ASZ Aalst, Aalst, Department of 3. Radiology UZ Gent, Ghent, Belgium Background: A 38-year-old male with no medical history complains about hemoptysis, chest pain, dyspnea on exertion and a cough. He has a history of occasional smoking, but had quitted smoking 1 year previously. There is a normal saturation and normal spirometry. Clinical examinatio...
متن کاملMounier-Kuhn syndrome.
Mounier-Kuhn syndrome, or tracheobronchomegaly, is a rare clinical entity characterized by abnormal dilation of the trachea and main bronchi. The diagnosis can usually be made by measuring the tracheal diameter. We report the case of a 40-year-old black man with refractory lower respiratory tract infection. Tracheobronchomegaly was confirmed through computed tomography.
متن کاملAnesthetic considerations for bilateral lung transplantation in Mounier-Kuhn syndrome.
MOUNIER-KUHN SYNDROME (MKS), or tracheobronchomegaly, is a rare disorder of unknown etiology that is characterized by marked dilation of the trachea and major bronchi, due to severe atrophy and thinning, as well as absence of elastic fibers and smooth muscular fibers of the large airways. This syndrome commonly presents in men in the third or fourth decade of life. It is marked by weakness of t...
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ژورنال
عنوان ژورنال: Critical Care Medicine
سال: 2020
ISSN: 0090-3493
DOI: 10.1097/01.ccm.0000730020.71604.d8